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propionyl CoA carboxylase (ATP-hydrolyzing) MeSH Supplementary Concept Data 2024


MeSH Supplementary
propionyl CoA carboxylase (ATP-hydrolyzing)
Unique ID
C022458
RDF Unique Identifier
http://id.nlm.nih.gov/mesh/C022458
Entry Term(s)
PCC (ATP-hydrolyzing)
propionyl coenzyme A carboxylase (ATP-hydrolyzing)
Registry Number
EC 6.4.1.3
Related Numbers
9023-94-3
Previous Indexing
*LIGASES (73-97)
ACYL COA (73-80)
COENZYME A (73-78)
PROPIONATES (73-80)
Heading Mapped to
*Carbon-Carbon Ligases
Frequency
71
Note
deficiency results in propionic acidemia; see also propionyl-CoA carboxylase (EC 4.1.1.41)
Source
Am J Hum Genet 1980;32(1):16
Am J Hum Genet 30(5):455;1978
Anal Biochem 52(1):305;1973
Biochem Genet 1979;17(7-8):703
Biochem Med 20(1):1;1978
Clin Chim Acta 100(2):183;1980
Clin Chim Acta 1980;101(2-3):217
Clin Chim Acta 76:321;1977
Clin Sci 1980;58(1):111
Enzyme 24(5):302;1979
J Biol Chem 252(23):8338;1977
J Biol Chem 254(13):5888;1979
J Biol Chem 255(1):236;1980
J Biol Chem 255(1):60;1980
J Clin Invest 64(6):1695;1979
J Inherit Metab Dis 1(1):3;1979
J Nutr 107(2):330;1977
Pediatr Res 9(7):559;1975
Pediatrics 1980;65(1):107
Postepy Biochem 25(2):141;1979
Poult Sci 56(6):1900;1977
Proc Natl Acad Sci USA 76(1):214;1979
Prog Food Nutr Sci 2(9):427;1977
Date of Entry
1973/01/01
Revision Date
2000/11/03
propionyl CoA carboxylase (ATP-hydrolyzing) Preferred
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